The second edition of Textbook of Systemic Vasculitis expands the scope and strengths of popular first edition of this book. This edition includes some newer topics like deficiency of adenosine deaminase 2 (DADA2),VEXAS syndrome, and other autoinflammatory vasculitides. The histopathology section has a new addition in the form of gastrointestinal (GI) vasculitis. There are invaluable insights into genetics, epidemiology, basic sciences including animal models, pathogenesis, and revised nomenclature systems, imaging modalities such as PET scan, disease activity assessment tools, and promising newer therapies.

• Covers new topics like DADA2 and VEXAS.
• Six sections devoted to different aspects of systemic vasculitides.
• In-depth introduction to epidemiology, classification, and genetics of systemic vasculitides.
• Role of neutrophils, antineutrophil cytoplasmic antibodies, and details of skin, nerves and brain, lungs, and kidney pathology.
• Imaging modalities as they have assumed a significant role in diagnosing and assessing disease activity.
• Detailed clinical manifestations based upon organ system or individual vasculitis syndromes.
• Approach to children and adults with vasculitis and assessing disease activity and damage.
• Newer and future treatment modalities.